Juvenile xanthogranuloma
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References
Juvenile xanthogranuloma (JXG) jẹ ipo ti o wọpọ ati iru loorekoore ti non-Langerhans cell histiocytic disorder ninu awọn ọmọde. Ni iwọn 75% awọn iṣẹlẹ, awọn ọgbẹ wọnyi han laarin ọdun akọkọ ti igbesi aye, ati pe o ju 15-20% ti awọn alaisan ni wọn lati ibimọ. Lakoko ti o ṣọwọn ninu awọn agbalagba, JXG maa n waye nigbagbogbo ni awọn eniyan ti o wa ni ọdun 20 si ọgbọn ọdun, ati ọpọlọpọ awọn alaisan agbalagba ni ọgbẹ kan. Ni ile-iwosan, o han bi ẹyọkan tabi ọpọ ofeefee-osan-brown duro bumps tabi lumps, nipataki lori oju, ọrun, ati ara oke. Awọn egbo ẹnu ko wọpọ ṣugbọn o le han bi odidi ofeefee ni awọn ẹgbẹ ahọn tabi ibomiiran ni ẹnu, o ṣee ṣe yori si ọgbẹ ati ẹjẹ. Awọn egbo awọ ara nigbagbogbo ko fa awọn aami aisan ati ṣọ lati lọ si ara wọn ni ọpọlọpọ ọdun. Botilẹjẹpe o ṣọwọn, ilowosi oju jẹ ọran ti o wọpọ julọ ju awọ ara lọ, ti o tẹle pẹlu ilowosi ẹdọfóró. Ocular JXG maa n kan oju kanṣoṣo ati pe o waye ni o kere ju 0. 5 % ti awọn alaisan, botilẹjẹpe nipa 40% ti awọn ti o ni ipa ocular tun ni awọn ọgbẹ awọ ara pupọ nigbati a ṣe ayẹwo.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranulomas (JXGs) ko wọpọ, awọn arun alaiṣe ti o jẹ apakan ti ẹka nla ti non-Langerhans cell histiocytoses. Wọn ṣe afihan nigbagbogbo bi ọkan tabi diẹ ẹ sii pupa tabi awọn lumps ofeefee, nigbagbogbo ti a rii ni ori tabi ọrun. Pupọ JXGs ni idagbasoke boya ni ibimọ tabi laarin ọdun akọkọ ti igbesi aye. Lakoko ti o jẹ dani, nigbami wọn le ni ipa awọn agbegbe ti o kọja awọ ara, pẹlu ilowosi oju jẹ nkan lati wo fun gẹgẹ bi awọn iwe ti o wa tẹlẹ. Ni gbogbogbo, awọn JXG lori awọ ara lọ kuro funrara wọn ati ni igbagbogbo ko nilo itọju.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Egbo oju farahan ni to 10% ti awọn eniyan pẹlu JXG ati pe o le ni ipa lori iran wọn. Botilẹjẹpe awọn egbo awọ-ara maa n parẹ lairotẹlẹ, awọn egbo oju o ṣọwọn ni ilọsiwaju lairotẹlẹ ati nilo itọju.